Myeloproliferative neoplasms (Registro nro. 22856)

000 -Cabecera
Campo de control interno 02005nam a2200253 4500
001 - Número de control
control field ESSALUD
005 - Fecha y hora de la última transacción
Campo de control 20260821144938.0
007 - Tipo material - Descripcion fisica - info general
Tipo material - Descripcion fisica - info general ta
008 - Elementos de Longitud Fija - Información General
Elementos de Longitud Fija - Información t pe ||||| |||| 00| 0 spa d
040 ## - Origen de la Catalogación
Origen de la Catalogación BMG
041 ## - Idioma
Idioma eng
100 ## - Autor
Autor Plo, Isabelle
Rol del Autor Autor
9 (RLIN) 54275
245 ## - Titulo
Titulo Myeloproliferative neoplasms
300 ## - Páginas
Paginación páginas: 788-802
520 ## - Resumen
Resumen Classic myeloproliferative neoplasms, including essential thrombocythemia, polycythemia vera, and primary myelofibrosis, are chronic, clonal hematopoietic stem-cell disorders. These disorders are driven by gain-of-function mutations in the genes Janus kinase 2 (JAK2), calreticulin (CALR), or the thrombopoietin receptor (MPL) that activate cytokine signaling. These mutations arise decades before clinical disease develops and confer a clonal advantage that is further shaped by comutations in epigenetic, splicing, or signaling genes. Inflammation enhances clonal dominance, favoring the development of myelofibrosis and thrombotic complications. Disease evolution may culminate in secondary acute myeloid leukemia, which has a poor prognosis. Current therapies primarily aim to control symptoms, thrombosis, and splenomegaly, but they have limited disease-modifying effects, except for pegylated interferon alfa and JAK2 inhibitors in some patients. Emerging therapies that selectively target mutant CALR and JAK2 V617F using immunotherapy and selective inhibitors could be a breakthrough in the treatment of persons with myeloproliferative neoplasms, with the expectation of achieving durable disease modification and potentially clonal eradication.
650 ## - Temas - Descriptores
Temas - Descriptores CÁNCER
9 (RLIN) 1231
650 ## - Temas - Descriptores
Temas - Descriptores TRATAMIENTOS EN ONCOLOGÍA
9 (RLIN) 53734
650 ## - Temas - Descriptores
Temas - Descriptores ENFERMEDAD INFLAMATORIA
9 (RLIN) 53667
650 ## - Temas - Descriptores
Temas - Descriptores LEUCEMIA
9 (RLIN) 33873
650 ## - Temas - Descriptores
Temas - Descriptores LINFOMA
9 (RLIN) 39360
700 ## - Autor Personal
Autor Personal Vainchenker, William
9 (RLIN) 54276
773 0# - Revista (Relacion con el numero)
Host Biblionumber 22717
Host Itemnumber 22650
Ciudad, Editorial Massachusetts NEJM Group
Codigo barras item/ejemplar NEJM12
Titulo de la Revista The New England Journal of Medicine
Número de control de registro ESSALUD
ISSN 0028-4793
942 ## - Elementos de Koha
Tipo de Documento Artículos
Fecha procesamiento 2026-08-21
Catalogador sqb

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